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G71.11

G71.11Myotonic muscular dystrophy

Billable / specific codeICD-10-CM

G71.11 is a billable, specific ICD-10-CM code for myotonic muscular dystrophy. It is valid for submission on a claim.

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

  • Dystrophia myotonica [Steinert]
  • Myotonia atrophica
  • Myotonic dystrophy
  • Proximal myotonic myopathy (PROMM)
  • Steinert disease

Other codes that can never be billed with G71.11

These codes carry an Excludes1 note pointing at G71.11. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading G71.11 alone.

  • E31Polyglandular dysfunction

Risk adjustment

G71.11 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 197 Muscular Dystrophy0.426 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

G71.11 is named in 23 Medicare coverage policies 23 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A52494High Frequency Chest Wall Oscillation Devices - Policy Article
  • A52510Mechanical In-exsufflation Devices - Policy Article
  • A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography
  • A52850Billing and Coding: Cardiac Catheterization and Coronary Angiography

How G71.11 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to G71.11.

  • Batten-Steinert syndrome
  • Curschmann disease or syndrome(-Batten) (-Steinert)
  • Steinert's disease
  • Atrophy, atrophicmyotonia
  • Disease, diseasedBatten-Steinert
  • Disease, diseasedCurschmann
  • Disease, diseasedSteinert's
  • Dystrophy, dystrophiamyotonic, myotonica
  • Myopathymytonic, proximal(PROMM)
  • Myopathyproximal myotonic(PROMM)
  • Myotoniaatrophica
  • Myotoniadystrophica

Related codes at this level

Codes that share G71.1. If G71.11 is not quite right, the correct code is usually one of these.

Questions about G71.11

Is G71.11 a billable ICD-10-CM code?
Yes. G71.11 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does G71.11 sit in the tabular list?
Diseases of the nervous system (G00-G99), in the block Diseases of myoneural junction and muscle (G70-G73).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.