Is G71.3 a billable ICD-10-CM code?

Yes. G71.3 is a billable, specific ICD-10-CM code and is valid for submission on a claim.

Where does G71.3 sit in the tabular list?

Diseases of the nervous system (G00-G99), in the block Diseases of myoneural junction and muscle (G70-G73).

What cannot be coded together with G71.3?

G71.3 carries an Excludes1 note, which means the conditions it lists can never be coded together with it on the same encounter.

G71.3

G71.3 — Mitochondrial myopathy, not elsewhere classified

Billable / specific codeICD-10-CM

G71.3 is a billable, specific ICD-10-CM code for mitochondrial myopathy, not elsewhere classified. It is valid for submission on a claim.

Excludes1 — never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

Kearns-Sayre syndrome (H49.81)
Leber's disease (H47.21)
Leigh's encephalopathy (G31.82)
mitochondrial metabolism disorders (E88.4.-)
Reye's syndrome (G93.7)

Other codes that can never be billed with G71.3

These codes carry an Excludes1 note pointing at G71.3. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading G71.3 alone.

E88.4Mitochondrial metabolism disorders

Risk adjustment

G71.3 does not map to an HCC and does not risk-adjust under CMS-HCC V28. That is normal — most ICD-10 codes do not. It still needs to be coded correctly; it just will not move a RAF score.

Medicare coverage

G71.3 is named in 12 Medicare coverage policies — 12 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

A52494High Frequency Chest Wall Oscillation Devices - Policy Article
A52510Mechanical In-exsufflation Devices - Policy Article
A54095Billing and Coding: Nerve Conduction Studies and Electromyography
A54095Billing and Coding: Nerve Conduction Studies and Electromyography

How G71.3 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to G71.3.

Myopathy›mitochondrial NEC

Related codes at this level

Codes that share G71. If G71.3 is not quite right, the correct code is usually one of these.

Questions about G71.3

Is G71.3 a billable ICD-10-CM code?: Yes. G71.3 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does G71.3 sit in the tabular list?: Diseases of the nervous system (G00-G99), in the block Diseases of myoneural junction and muscle (G70-G73).
What cannot be coded together with G71.3?: G71.3 carries an Excludes1 note, which means the conditions it lists can never be coded together with it on the same encounter.