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ICD-10-CM tabular list

Q50-Q56Congenital malformations of genital organs

ICD-10-CM codes Q50-Q56 cover congenital malformations of genital organs, within congenital malformations, deformations and chromosomal abnormalities. The block holds 115 codes across 7 categories, of which 91 are billable and 24 are header codes that cannot be submitted on a claim.

Excludes1 — never code together

These conditions cannot occur together. Billing both on the same encounter is a denial.

  • androgen insensitivity syndrome (E34.5-)
  • syndromes associated with anomalies in the number and form of chromosomes (Q90-Q99)

What else to watch in Q50-Q56

  • 4 codes are laterality-specific. They come in left and right pairs, and the pair is mutually exclusive on a single site: coding both without a bilateral code is a contradiction a scrubber should catch before the payer does.
  • 46 codes are named in Medicare coverage policies. An LCD or NCD lists them as supporting medical necessity, or explicitly as not supporting it. Which applies depends on the MAC for your state.

Categories in Q50-Q56

ICD-10-CMFY2026-Apr· effective April 1, 2026