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E83.01

E83.01Wilson's disease

Billable / specific codeICD-10-CM

E83.01 is a billable, specific ICD-10-CM code for wilson's disease. It is valid for submission on a claim.

Code also

Both codes may be needed to describe the encounter fully. Sequencing depends on the reason for the visit.

  • associated Kayser Fleischer ring (H18.04-)

Risk adjustment

E83.01 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 50 Amyloidosis, Porphyria, and Other Specified Metabolic Disorders0.648 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

E83.01 is named in 3 Medicare coverage policies 3 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A56199Billing and Coding: Molecular Pathology Procedures
  • A56868Billing and Coding: Outpatient Speech Language Pathology
  • A60409Billing and Coding: Molecular Pathology Procedures

How E83.01 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to E83.01.

  • Hepatolenticular degeneration
  • Kinnier Wilson's disease(hepatolenticular degeneration)
  • Lenticular degeneration, progressive
  • Strümpell-Westphal pseudosclerosis
  • Westphal-Strümpell syndrome
  • Deficiency, deficientceruloplasmin(Wilson)
  • Degeneration, degenerativehepatolenticular(Wilson's)
  • Degeneration, degenerativelenticular(familial) (progressive) (Wilson's) (with cirrhosis of liver)
  • Degeneration, degenerativeWilson's hepatolenticular
  • Disease, diseasedhepatolenticular
  • Disease, diseasedKinnier Wilson's(hepatolenticular degeneration)
  • Disease, diseasedWilson's(hepatolenticular degeneration)

Related codes at this level

Codes that share E83.0. If E83.01 is not quite right, the correct code is usually one of these.

Questions about E83.01

Is E83.01 a billable ICD-10-CM code?
Yes. E83.01 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does E83.01 sit in the tabular list?
Endocrine, nutritional and metabolic diseases (E00-E89), in the block Metabolic disorders (E70-E88).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.