Is G11.3 a billable ICD-10-CM code?

Yes. G11.3 is a billable, specific ICD-10-CM code and is valid for submission on a claim.

Where does G11.3 sit in the tabular list?

Diseases of the nervous system (G00-G99), in the block Systemic atrophies primarily affecting the central nervous system (G10-G14).

G11.3

G11.3 — Cerebellar ataxia with defective DNA repair

Billable / specific codeICD-10-CM

G11.3 is a billable, specific ICD-10-CM code for cerebellar ataxia with defective dna repair. It is valid for submission on a claim.

Excludes2 — not included here, but may coexist

The excluded condition is not part of this code, but a patient can have both. You may code both.

Cockayne's syndrome (Q87.19)
other disorders of purine and pyrimidine metabolism (E79.-)
xeroderma pigmentosum (Q82.1)

Inclusion terms

Alternative wordings a physician may use in the chart for this same code.

Ataxia telangiectasia [Louis-Bar]

Other codes that can never be billed with G11.3

These codes carry an Excludes1 note pointing at G11.3. The conflict binds both ways, but ICD-10-CM only writes it down on one side — so you would not find this by reading G11.3 alone.

Q85Phakomatoses, not elsewhere classified
D82Immunodeficiency associated with other major defects
E31Polyglandular dysfunction

Risk adjustment

G11.3 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

HCC 200 Friedreich and Other Hereditary Ataxias; Huntington Disease0.279 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

G11.3 is named in 27 Medicare coverage policies — 27 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

A52507External Infusion Pumps - Policy Article
A52509Intravenous Immune Globulin - Policy Article
A53057Billing and Coding: Home Health Occupational Therapy
A53064Billing and Coding: Outpatient Occupational Therapy

How G11.3 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to G11.3.

Ataxia-telangiectasia(Louis-Bar)
Boder-Sedgwick syndrome(ataxia-telangiectasia)
Louis-Bar syndrome(ataxia-telangiectasia)
Ataxia, ataxy, ataxic›telangiectasia(Louis-Bar)
Syndrome›ataxia-telangiectasia
Syndrome›Boder-Sedgewick
Syndrome›Louis-Barré
Telangiectasia, telangiectasis›ataxic(cerebellar) (Louis-Bar)
Ataxia, ataxy, ataxic›cerebellar›with defective DNA repair

Related codes at this level

Codes that share G11. If G11.3 is not quite right, the correct code is usually one of these.

Questions about G11.3

Is G11.3 a billable ICD-10-CM code?: Yes. G11.3 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does G11.3 sit in the tabular list?: Diseases of the nervous system (G00-G99), in the block Systemic atrophies primarily affecting the central nervous system (G10-G14).