MCMCB Pro
D47.Z2

D47.Z2Castleman disease

Billable / specific codeICD-10-CM

D47.Z2 is a billable, specific ICD-10-CM code for castleman disease. It is valid for submission on a claim.

Excludes2 — not included here, but may coexist

The excluded condition is not part of this code, but a patient can have both. You may code both.

  • Kaposi's sarcoma (C46.-)

Code also

Both codes may be needed to describe the encounter fully. Sequencing depends on the reason for the visit.

  • , if applicable, human herpesvirus 8 infection (B10.89)

Risk adjustment

D47.Z2 risk-adjusts. Under the CMS-HCC V28 model it maps to this category:

  • HCC 21 Lymphoma and Other Cancers0.671 RAF

Coefficient shown for the Community Non-dual Aged segment. A higher HCC in the same hierarchy will suppress this one, so capturing it does not always add score.

Medicare coverage

D47.Z2 is named in 18 Medicare coverage policies 18 listing it as supporting medical necessity. Which of them applies to you depends on your Medicare contractor, and coverage genuinely differs by state.

  • A52480Oral Antiemetic Drugs (Replacement for Intravenous Antiemetics) - Policy Article
  • A54768Billing and Coding: Cardiac Blood Pool Imaging (Multiple Gated Acquisition Scanning- MUGA, Ventriculography) When Performed in Conjunction with Cardiotoxic Chemotherapy
  • A55336Billing and Coding: Retroperitoneal Ultrasound
  • A55717Billing and Coding: Lab: Flow Cytometry

How D47.Z2 is indexed

Coders do not find codes by browsing the tabular list — they look them up in the alphabetic index, under the word the physician wrote. These are the index entries that lead here, so you can see which chart wordings map to D47.Z2.

  • Disease, diseasedCastleman(unicentric) (multicentric)
  • Disease, diseasedCastlemanHHV-8-associated

Related codes at this level

Codes that share D47.Z. If D47.Z2 is not quite right, the correct code is usually one of these.

Questions about D47.Z2

Is D47.Z2 a billable ICD-10-CM code?
Yes. D47.Z2 is a billable, specific ICD-10-CM code and is valid for submission on a claim.
Where does D47.Z2 sit in the tabular list?
Neoplasms (C00-D49), in the block Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes (D37-D48).
ICD-10-CMFY2026-Apr· effective April 1, 2026

Loaded directly from the CMS/NCHS ICD-10-CM public-domain release — see data sources and our editorial policy. If this page disagrees with the CMS tabular list, this page is wrong. Reference information for professional coders; not medical or billing advice.